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[Right aortic arch associated with congenital heart defects]
Archivos Del Instituto De Cardiologia De Mexico
|March 1, 1978
Summary
Right aortic arch is found in 4.6% of congenital heart defects, most commonly associated with Tetralogy of Fallot. This condition is not linked to certain other heart malformations.
Area of Science:
- Cardiovascular Medicine
- Pediatric Cardiology
- Medical Genetics
Context:
- Congenital cardiac malformations represent a significant area of pediatric health concern.
- Understanding the variations in aortic arch development, such as a right aortic arch, is crucial for diagnosing associated cardiac anomalies.
Purpose:
- To report on the association between right aortic arch and various congenital cardiac malformations based on clinical experience.
- To analyze the frequency and specific types of congenital heart defects associated with right aortic arch.
Summary:
- A study of 1200 congenital cardiac malformations identified 56 cases (4.6%) with a right aortic arch.
- Type I right aortic arch was predominant (96%) and frequently associated with Tetralogy of Fallot (46%), transposition of the great vessels (14.3%), truncus arteriosus (12%), tricuspid atresia (10.7%), and visceral heterotaxy (10.7%).
- Rarely observed Type II and Type III right aortic arches were linked to pulmonary valvular stenosis, atrial septal defect, and ventricular septal defect, with no association found with total anomalous pulmonary venous return or mitral/aortic valvular malformations.
Impact:
- Provides valuable data on the prevalence and specific associations of right aortic arch in congenital heart disease.
- Aids in refining diagnostic approaches and understanding the spectrum of anomalies linked to right aortic arch.
- Contributes to the knowledge base for genetic counseling and management strategies for affected children.