Malignant abdominal schwannoma associated with von Recklinghausen's neurofibromatosis

A 4-year-old boy with neurofibromatosis was operated on for abdominal tumor and a malignant Schwannoma adhering to the bladder was completely resected. Four months later he died with multiple liver metastases. The authors comment on the main features of this rate tumor and on the problems of malignancy associated with von Recklinghausen's disease.