[Origin of the right pulmonary artery from the ascending aorta]

A 19-day old female infant presented with congestive cardiac failure. Cardiac catheterization and angiography demonstrated the right pulmonary artery to originate from the ascending aorta, and an atrial septal defect with a left to right shunt of 40%. At the age of six months anastomosis of the right pulmonary artery to the main pulmonary artery was performed with hypothermic arrest and cardioplegia. The postoperative course was complicated by respiratory distress but later the patient's condition improved. Four years later control cardiac catheterization and angiography visualized operative repair and only a small left to right shunt of 20% at atrial level.