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[Liver diseases with microsomal antibodies. Frequency, clinical and immunological findings and course observations

Zeitschrift Fur Gastroenterologie
|August 1, 1978
PubMed

Insights

Liver kidney microsomal antibodies (LKM-antibodies) are rare humoral autoantibodies. A study found LKM-antibodies in 6.9% of pediatric liver disease cases, suggesting a role in chronic hepatitis.

Area of Science:

  • Autoimmunology
  • Hepatology
  • Nephrology

Background:

  • Microsomal antibodies (LKM-antibodies) are rare humoral autoantibodies distinct from mitochondrial antibodies.
  • LKM-antibodies target hepatocytes and renal tubules, unlike antibodies that stain parietal cells.

Observation:

  • A prospective study analyzed 930 adults and 33 children with chronic hepatitis or cirrhosis.
  • LKM-antibodies were detected in 0.38% of adults and 6.9% of children with liver diseases.

Findings:

  • Six patients (3 children, 3 adults) with LKM-antibodies and chronic active hepatitis were identified.
  • Two children with LKM-antibodies developed inactive postnecrotic cirrhosis despite initial rapid progression.

Implications:

  • LKM-antibodies are more prevalent in pediatric liver disease than in adults.
  • The clinical course associated with LKM-antibodies can vary, even leading to cirrhosis in some cases.

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