[Is the BK mole syndrome always an autosomal dominant trait?]

After a brief review of the characteristics of familial malignant melanoma, the authors summarize the literature about the BK mole syndrome. The clinical and histological features of this dermatosis are described. Three personal cases are also reported. The latter tend to demonstrate a certain genetic heterogeneity, while in the literature the BK mole syndrome has been described as an autosomal dominant trait.