[Juvenile nevoxanthogranuloma of the iris]

Juvenile Xanthogranuloma of the iris is a rare but benign disease of infants. The iris is swollen and of yellowish color, there are exsudates in the anterior chamber and occasionally spontaneous hyphema may occur. Secondary glaucoma with edema of the corneal epithelium and hydrophthalmus are often seen. Treatment consists in topical application of steroids, sometimes combined with pressure-lowering medication.