Phrenicus palsy in progressive systemic sclerosis

We report the course of a patient with progressive systemic sclerosis (PSS), who died of respiratory failure. Her condition was aggravated by the terminal development of unilateral Phrenicus palsy (PP), which has not previously been reported among the multiple presentations of scleroderma. PP should be borne in mind as one of the potential causes of decreasing lung function in scleroderma.