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[Localized recurrent light-induced Darier disease following Blaschko lines]
P Plantin1, E Le Noac'h, J P Leroy
1Service de Dermatologie, CH de Cornouaille, Quimper.
Annales De Dermatologie Et De Venereologie
|January 1, 1994
Summary
Localized Darier's disease can be photo-induced. This case report details a patient with a linear eruption, confirmed as Darier's disease, triggered by UVB light.
Area of Science:
- Dermatology
- Genetics
Background:
- Darier's disease is a rare genetic skin disorder.
- Localized variants present unique diagnostic challenges.
- Photo-induced exacerbations are not widely reported.
Observation:
- A patient presented with a ten-year history of a linear eruption recurring annually during summer.
- Clinical and photological examinations revealed acantholytic dyskeratosis consistent with Darier's disease.
- UVB phototests successfully reproduced the lesions, indicating photo-sensitivity.
Findings:
- The case supports localized Darier's disease.
- The linear eruption pattern suggests cutaneous mosaicism.
- UVB radiation specifically triggers lesions, distinct from Koebner phenomenon.
Implications:
- Highlights the importance of considering photo-sensitivity in Darier's disease.
- Suggests UVB phototesting as a diagnostic tool for photo-induced dermatoses.
- Advances understanding of Darier's disease variants and their triggers.