Multiple peripheral pulmonary artery branch stenosis in a young Japanese girl with systemic hypertension

We present a 16-year-old girl with pulmonary hypertension due to multiple pulmonary artery obstructions and stenoses. Juvenile hypertension was complicated by 75 percent stenosis of the left renal artery. Similar pulmonary angiographic findings 1 year later and no sign of inflammation in the following year suggest that this condition is congenital in origin.