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[West syndrome: apropos of 9 cases]
M A Kamiyama1, L Yoshinaga, E R Tonholo-Silva
1Hospital de Clínicas da Faculdade de Medicina de Marília (FMM), Brasil.
Arquivos De Neuro-Psiquiatria
|September 1, 1993
Abstract:
West syndrome is a peculiar form of epilepsy of infancy and childhood characterized by spasms or massive myoclonus, regression neuropsychomotor development, and EEG abnormalities referred as hipsarrhythmia. We report nine cases of West syndrome discussing clinical, etiological, evolutive and therapeutic features.