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Published on: February 11, 2022
Cardiac surgery with extracorporeal circulation in severe factor VII deficiency
A Ferster1, V Capouet, A Deville
1Department of Haematology, Hôpital Universitaire des Enfants Reine Fabiola, Free University Brussels (ULB), Belgium.
Abstract:
We describe here successful open heart surgery with extracorporeal circulation and haemodilution in a child with severe congenital factor VII deficiency. Substitution therapy was realized with factor VII concentrate (SD proconvertin concentrate, Bio-Transfusion). This is the first report case of successful cardiac surgery in severe congenital factor VII deficiency.
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