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Acquired C1 inhibitor deficiency revealing systemic lupus erythematosus
S Ochonisky1, L Intrator, J Wechsler
1Service de Dermatologie, Hôpital Henri-Mondor, Créteil, France.
Dermatology (Basel, Switzerland)
|January 1, 1993
Abstract:
We report the case of a previously healthy 54-year-old woman, without any family history, who developed an angioneurotic edema with acquired C1 inhibitor deficiency and systemic lupus erythematosus. The search for a lymphoproliferative disorder was negative. Hydroxychloroquine therapy induced simultaneous resolution of lupus and angioedema. The pathophysiology of this association is discussed.