Complete dentures for a child with hypohidrotic ectodermal dysplasia: a clinical report

Area of Science:

• Pediatric Dentistry
• Craniofacial Anomalies
• Genetics

Background:

• Hypohidrotic ectodermal dysplasia (HED) is a rare genetic disorder characterized by abnormal development of ectodermal structures, including teeth, hair, and sweat glands.
• Anodontia, the congenital absence of teeth, significantly impacts a child's oral function, speech, and psychosocial well-being.
• Early intervention with prosthodontic rehabilitation is crucial for the holistic development of children with HED.

Observation:

• Young children with HED experience challenges with eating, speech, and social integration due to missing teeth and altered appearance.
• The desire for a normal appearance and the ability to socialize with peers can be powerful motivators for cooperation in young children during dental treatment.
• Successful denture fabrication is achievable even in young children, provided there is good patient cooperation and multiple appointments.

Findings:

• Well-fitting, functional dentures with age-appropriate teeth can significantly improve the quality of life for children with HED.
• The process of denture fabrication, while requiring multiple appointments, can be managed successfully with young pediatric patients.
• Cooperation from young children during dental procedures can be fostered by explaining the benefits of having teeth and addressing their desire to resemble their peers.

Implications:

• Pediatric dentists play a vital role in the comprehensive care of children with HED, contributing to their overall development and well-being.
• Prosthodontic rehabilitation can enhance the functional and esthetic outcomes for children with anodontia, facilitating their transition into school and social environments.
• Addressing the dental needs of children with HED supports their potential to develop fully and improves their long-term psychosocial adjustment.