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Hematopoietic cell protein-tyrosine phosphatase-deficient motheaten mice exhibit T cell apoptosis defect

X Su1, T Zhou, P A Yang

  • 1Department of Medicine, the University of Alabama at Birmingham, AL 35294, USA.

Insights

Hematopoietic cell protein-tyrosine phosphatase deficiency impairs Fas-mediated apoptosis in T cells, leading to lymphoproliferative disease and tissue infiltration in mice.

Area of Science:

  • Immunology
  • Cell Biology
  • Molecular Biology

Background:

  • Hematopoietic cell protein-tyrosine phosphatase (HCPTP) transduces Fas-mediated apoptosis signals in lymphoid cells.
  • Defective Fas signaling impacts T cell phenotype and function.

Purpose of the Study:

  • To analyze the effects of defective Fas signaling on T cell phenotype and apoptosis in HCPTP-deficient motheaten mice.
  • To investigate the mechanism of Fas-mediated apoptosis resistance in these mice.

Main Methods:

  • Analysis of T cell proliferation and apoptosis in viable motheaten (me(v)/me(v)) mice.
  • Assessment of Fas ligand function.
  • Confirmation of Fas-mediated apoptosis defect via anti-Fas-induced apoptosis assays.
  • Evaluation of protein tyrosine dephosphorylation after anti-Fas cross-linking using 32Pi labeling.
  • Characterization of T cell populations (CD4, CD8, B220, CD3) and cell cycling (bromodeoxyuridine uptake).

Main Results:

  • me(v)/me(v) mice showed increased T cell proliferation and defective activation-induced apoptosis of Fas+ T cells.
  • Resistance to anti-Fas-induced apoptosis was observed in activated T cells from me(v)/me(v) mice.
  • No protein tyrosine dephosphorylation signal occurred after anti-Fas cross-linking in me(v)/me(v) lymph node cells.
  • Defective apoptosis led to lymphadenopathy with accumulation of CD4- CD8- B220+ CD3+ T cells.
  • Pneumonitis was associated with infiltration of cycling T cells.

Conclusions:

  • T cells from me(v)/me(v) mice are resistant to Fas-mediated apoptosis.
  • This resistance results in lymphoproliferative disease and tissue infiltration.
  • HCPTP plays a crucial role in transducing Fas-mediated apoptosis signals in T cells.

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