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An audit of sickle cell screening in a paediatric hospital population

A Baraka1, G Haddock, X Roussis

  • 1Department of Paediatric Surgery, Royal Hospital for Sick Children, Yorkhill, Glasgow.

Insights

UK sickle cell disease (SSD) screening guidelines are costly. A retrospective audit found a low incidence of SSD in a diverse patient population, suggesting selective screening may be more cost-effective for certain ethnic groups.

Area of Science:

  • Hematology
  • Public Health

Background:

  • Current UK guidelines recommend pre-operative sickle cell disease (SSD) screening for specific ethnic groups.
  • These guidelines have significant cost implications for the National Health Service (NHS).

Purpose of the Study:

  • To retrospectively audit the utilization and outcomes of SSD screening in a UK institution.
  • To evaluate the cost-effectiveness of current SSD screening protocols.

Main Methods:

  • Retrospective audit of 1305 patients under 15 years old screened for SSD between January 1987 and August 1992.
  • Analysis of patient ethnicity and screening test results.

Main Results:

  • 85.8% of tests were performed on surgical patients.
  • The majority of tested patients were of Asian descent (73%), with 27% of African or Afro-Caribbean descent.
  • Only four patients (0.3%) tested positive for sickle cell trait; three were of Afro-Caribbean descent and one from Bahrain.

Conclusions:

  • The incidence of sickle cell hemoglobin (HbS) is low in the studied population.
  • Continued SSD testing for patients of African or Afro-Caribbean descent is supported.
  • A selective screening policy may be appropriate for other ethnic groups to improve cost-effectiveness.

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