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Vasculitis and lymphoproliferative diseases

M D Wooten1, H E Jasin

  • 1Department of Internal Medicine, University of Arkansas for Medical Sciences, Little Rock 72205, USA.

Seminars in Arthritis and Rheumatism
|October 1, 1996
PubMed
Summary

Vasculitis is an uncommon complication of lymphoproliferative diseases. Early screening for these cancers is crucial in patients presenting with vasculitis, as it may precede diagnosis.

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Area of Science:

  • Oncology
  • Rheumatology
  • Pathology

Background:

  • Vasculitis is an uncommon complication of lymphoproliferative diseases.
  • Cutaneous vasculitis is typically necrotizing and leukocytoclastic.
  • Granulomatous vasculitis and T-cell lymphocytic vasculitis with eosinophilia are rare associations.

Purpose of the Study:

  • To review the uncommon associations between vasculitis and lymphoproliferative diseases.
  • To highlight the importance of considering lymphoproliferative disorders in patients with vasculitis.

Main Methods:

  • Literature review of reported cases and associations between vasculitis and lymphoproliferative diseases.
  • Analysis of the types of vasculitis and specific lymphoproliferative disorders involved.

Main Results:

  • Cryoglobulinemia is the most common systemic vasculitis associated with lymphocytic lymphoma or Waldenström's macroglobulinemia.
  • Other rare associations include polyarteritis nodosa with hairy cell leukemia, Wegener's granulomatosis with Hodgkin's disease, and central nervous system vasculitis with lymphoma.
  • Vasculitis can manifest before the lymphoproliferative disease is diagnosed.

Conclusions:

  • Patients presenting with vasculitis should be screened for underlying lymphoproliferative diseases.
  • Monitoring patients with diagnosed lymphoproliferative diseases for the development of vasculitis is important.

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