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Cardiac surgery for Kartagener syndrome
T Tkebuchava1, L K von Segesser, U Niederhäuser
1Clinic for Cardiovascular Surgery, University Hospital, Zurich, Switzerland.
Pediatric Cardiology
|January 1, 1997
Summary
Children with Kartagener syndrome and heart defects can undergo successful cardiac surgery. Long-term outcomes show good physical activity and no need for heart medication.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Surgery
- Genetics and Rare Diseases
Background:
- Kartagener syndrome is a rare genetic disorder characterized by situs inversus, chronic sinusitis, and bronchiectasis.
- Patients with Kartagener syndrome may present with associated congenital cardiac anomalies, complicating management.
- Surgical intervention for congenital heart disease in these patients requires careful consideration due to potential pulmonary complications.