[Rare congenital heart valve defects]

The article contains excerpts from case records and autopsy protocols for two children who had died of congenital valvular heart diseases. Both were full-term infants, with good weight who initially developed normally. During the first month of life, however, they developed respiratory disease which provoked the development of decompensation of the malformed heart. Moreover, both patients showed clinical signs of congestion not only in the greater circulation but in the lesser circulation as well. The latter was conditioned by anatomic features of the valvular defects. In the first case all the valves of the heart turned out to be malformed, in the second case there was observed a combination of Ebstein's anomaly with corrected transposition of the ventricles and major vessels of the heart and as a result the right ventricle with a malformed tricuspid valve was found to be on the place of the left ventricle.