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[Acute pancreatitis in Caroli's syndrome]
R García Valriberas1, J Díaz Blasco, J A Moreno Monteagudo
1Servicio de Aparato Digestivo, Hospital La Princesa, Madrid.
Revista Espanola De Enfermedades Digestivas
|February 1, 1997
Summary
Caroli's syndrome, a bile duct abnormality, typically causes cholangitis. This case highlights its rare presentation as adult acute pancreatitis, necessitating liver transplantation.
Area of Science:
- Hepatology
- Gastroenterology
- Surgical Pathology
Background:
- Caroli's syndrome is a rare congenital fibropolycystic disease affecting the intrahepatic bile ducts.
- It is characterized by cystic dilatation of the bile ducts and is associated with other fibropolycystic liver diseases.
- The typical clinical manifestation is recurrent cholangitis, often leading to complications like liver abscesses and portal hypertension.