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Corneal abnormalities associated with incontinentia pigmenti
R C Ferreira1, L C Ferreira, L Forstot
1Department of Ophthalmology, Federal University of São Paulo.
American Journal of Ophthalmology
|April 1, 1997
Abstract
Purpose:
To report corneal abnormalities associated with incontinentia pigmenti.
Case Reports:
Two girls, aged 2 1/2 and 5 years, with incontinentia pigmenti from one family underwent a complete ophthalmic examination.
Results:
We found vortex (whorl-like) epithelial keratitis characterized by epithelial microcysts that stained with fluorescein and midstromal radial mild haziness in daughters of a family with incontinentia pigmenti.
Conclusion:
Incontinentia pigmenti should be included in the differential diagnosis of children with keratitis, particularly if there is evidence of characteristic dermatologic or other systemic manifestations.