Mandibulofacial dysostosis: surgical treatment

In six persons with mandibulofacial dysostosis, surgical correction of the anomaly was performed at different ages using different methods. In two persons between the ages of 7 and 9 years, correction of the zygomaticomaxillary region, using rib cartilage, was performed first. Later, at the age of 14 years, suitable orthognathic surgical procedures were done. In two patients at the ages of 16 and 17 years suitable orthognathic surgical procedures were performed first and correction of zygomaticomaxillary region, using rib cartilage, was performed 1 year later. In two 18-year-olds, the zygomaticomaxillary region was corrected using vascularized osteopericranial and additional pericranial flaps. In one of these two persons, suitable orthognathic surgical procedures had been performed a year before. The poorest results were obtained in two patients whose surgical treatment began at 7 to 9 years of age. The best results were obtained in those in whom suitable orthognathic surgical procedures were performed between 16 and 18 years of age with the correction of the zygomaticomaxillary region a year later.