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A case of pigmented dermatofibrosarcoma protuberans (Bednar tumor)
1Department of Dermatology, Iwate Medical University, School of Medicine, Morioka, Japan.
The Journal of Dermatology
|June 1, 1997
Summary
Pigmented dermatofibrosarcoma protuberans (Bednar tumor) is an intermediate malignant skin tumor, not benign. This rare variant shares features with common dermatofibrosarcoma protuberans, indicating it
Area of Science:
- Dermatopathology
- Oncology
Background:
- Dermatofibrosarcoma protuberans (DFSP) is a rare, locally aggressive skin cancer.
- Pigmented DFSP, also known as Bednar tumor, is a rare variant.
- Understanding the nature of Bednar tumor is crucial for accurate diagnosis and treatment.
Observation:
- A case of a 67-year-old male with a recurrent pigmented dermatofibrosarcoma protuberans on his right shoulder is presented.
- The lesion exhibited clinical features of a reddish-brown, exophytic, multilobular nodule measuring 6.4 x 4.2 cm.
- Histological examination revealed features consistent with DFSP, including CD34-positive fibroblasts in a cartwheel pattern, with intermingled S-100 positive melanin-bearing cells.
Findings:
- The clinical, histological, and cytological features, along with the presence of melanin-bearing dendritic cells, support DFSP.
- These findings suggest that pigmented DFSP is a pigmented variant of DFSP.
- The tumor is classified as an intermediate malignant tumor, not benign.
Implications:
- This case reinforces the classification of pigmented dermatofibrosarcoma protuberans as a variant of DFSP.
- Accurate classification is essential for appropriate patient management and prognosis.
- Further research into DFSP variants can improve understanding of skin cancer biology.