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Choledochal cyst in infancy: report of two cases
1Department of Pediatrics and Surgery, Cathay General Hospital, Taipei, Taiwan, R.O.C.
Zhonghua Minguo Xiao Er Ke Yi Xue Hui Za Zhi [Journal]. Zhonghua Minguo Xiao Er Ke Yi Xue Hui
|July 1, 1997
Summary
Congenital choledochal cysts, a rare infant biliary malformation, present with jaundice and acholic stools. Early diagnosis and surgical excision with Roux-en-Y reconstruction offer successful outcomes.
Area of Science:
- Pediatric Surgery
- Gastroenterology
- Medical Imaging
Background:
- Choledochal cysts are congenital biliary ductal malformations, rare in infancy, often presenting with cholestatic jaundice and acholic stools due to biliary obstruction.
- In neonates and infants, they are congenital and may associate with distal biliary atresia; in older individuals, they can be acquired, linked to anomalous pancreaticobiliary union.
Observation:
- Two infants, aged 9 and 7 weeks, presented with jaundice, acholic stools, and hepatomegaly, indicative of biliary obstruction.
- Diagnostic imaging, including sonography, computed tomography, and hepatobiliary scintigraphy, confirmed the presence of choledochal cysts in both patients.
Findings:
- Congenital choledochal cysts were diagnosed in two infants using a combination of imaging modalities.
- Both patients underwent successful surgical excision of the choledochal cysts followed by Roux-en-Y reconstruction of the biliary tree.
Implications:
- Early detection and surgical intervention are crucial for preventing fatal complications associated with biliary obstruction from choledochal cysts.
- Successful surgical outcomes highlight the importance of timely diagnosis and treatment in infants with congenital choledochal cysts.