Related Experiment Video
Updated: Jul 7, 2026
18:50
Microsurgical Clip Obliteration of Middle Cerebral Aneurysm Using Intraoperative Flow Assessment
Published on: September 25, 2009
[Scleroderma en coup de sabre with intracranial involvement. A case report]
A Ortigado Matamala1, M A Martínez Granero, I Pascual Castroviejo
1Servicio de Neurología Infantil, Hospital Infantil La Paz, Madrid.
Neurologia (Barcelona, Spain)
|June 1, 1997
Summary
Scleroderma en coup de sabre, a rare linear scleroderma, often affects children and can involve neurological issues like epilepsy. This case highlights that inflammation in this condition extends beyond the skin.
Area of Science:
- Dermatology
- Neurology
- Pediatrics
Background:
- Scleroderma en coup de sabre is a rare subtype of linear scleroderma affecting the face and scalp.
- It primarily impacts pediatric patients and is frequently associated with neurological complications, particularly epilepsy.
Observation:
- A 15-year-old female patient presented with scleroderma en coup de sabre and a history of epilepsy.
- Clinical examination suggested that the inflammatory process might extend beyond the cutaneous manifestations.
Findings:
- Cranial magnetic resonance imaging (MRI) was performed to investigate the extent of inflammation.
- The MRI results supported the clinical suspicion, indicating that inflammation was not limited to the skin in this case of linear scleroderma.
Implications:
- This case underscores the importance of considering neurological involvement in patients with scleroderma en coup de sabre.
- Further investigation into the neurocutaneous manifestations of this rare condition is warranted.
- Enhanced diagnostic approaches may be necessary to fully assess the extent of inflammation in scleroderma en coup de sabre.
