Uterine anomalies associated with unilateral renal agenesis

Six cases of concomitant uterine anomalies and absent kidney are reported. Five of these were obstructive in type, 2 representing a mother and daughter relationship. The importance of investigation of the genitourinary system in the presence of uterine anomaly is emphasized. Fertility is unimpaired but obstetric complications are common, especially premature delivery and breech presentation. Treatment can be simple--drainage of unilateral hematocolpos--but excision of the septum may be necessary. The abnormal embryonic development is reviewed.