The neuropathology of selected neurocutaneous diseases

The neurocutaneous diseases are a collection of more than 40 hereditary and spontaneously occurring disorders, many of which have prominent lesions involving the nervous system and skin. In this article, the classification of the neurocutaneous diseases is briefly reviewed, and the neuropathologic characteristics of four of these diseases (neurofibromatosis, tuberous sclerosis, von Hippel-Lindau disease, and Sturge-Weber disease) are summarized.