Coronary arteriovenous malformations in a patient with hereditary hemorrhagic telangiectasia--a case report

Y Gurevitch1, Y Hasin, M S Gotsman

  • 1Cardiology Department, Hadassah University Hospital, Ein Kerem, Jerusalem, Israel.

Angiology
|July 22, 1998
PubMed

Hereditary hemorrhagic telangiectasia (Osler-Weber-Rendu) disease is characterized by cutaneous, mucosal, and visceral vascular anomalies. Two patients were previously described with coronary artery aneurysms (ectasia) associated with this disease. This report describes a patient with Osler-Weber-Rendu disease in whom multiple coronary arteriovenous malformations were identified during coronary angiography. The patient presented with anginal chest pain resulting from severe anemia. Upper gastrointestinal endoscopy revealed multiple angiodysplastic lesions throughout the esophagus and stomach.

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