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Primitive neuroectodermal tumor of the lingual nerve: a case report
1Department of Pediatric Plastic and Reconstructive Surgery, Chang Gung Memorial Hospital, Taoyuan, Taiwan, ROC.
Changgeng Yi Xue Za Zhi
|September 8, 1998
Summary
This case report details a rare pediatric head and neck tumor, a primitive neuroectodermal tumor (PNET) of the lingual nerve. The child survived 12 months post-treatment, highlighting the need for aggressive management of these aggressive brain tumors.
Area of Science:
- Pediatric Oncology
- Neuropathology
- Head and Neck Surgery
Background:
- Primitive neuroectodermal tumors (PNETs) are rare in the pediatric head and neck region.
- PNETs originating from cranial nerves in children are exceptionally uncommon.
- Early diagnosis and treatment are crucial due to the aggressive nature of PNETs.
Observation:
- A case of a 5-year-old girl with a PNET arising from the lingual nerve is presented.
- The tumor was surgically excised, followed by postoperative chemotherapy.
- The patient was monitored for 12 months post-treatment.
Findings:
- The patient remained alive and showed no evidence of recurrence or metastasis at the 12-month follow-up.
- This represents the first reported case of a PNET originating from a cranial nerve in a child.
- The successful outcome underscores the potential efficacy of combined surgical and chemotherapeutic approaches.
Implications:
- PNETs should be considered in the differential diagnosis of pediatric head and neck masses.
- Aggressive surgical and medical treatment strategies are warranted for pediatric PNETs.
- This case contributes valuable data to the understanding and management of rare pediatric neuroectodermal tumors.