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Updated: Jul 31, 2026

Use of Ultra-high Field MRI in Small Rodent Models of Polycystic Kidney Disease for In Vivo Phenotyping and Drug Monitoring
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[Kniest's disease, (a familial case)]

D Gnamey, J P Farriaux, G Fontaine

    Archives Francaises De Pediatrie
    |February 1, 1976
    PubMed
    Summary

    Kniest's disease, a type of spondylo-epiphyseal dysplasia, was recently identified. This study details a second familial case, confirming its transmission as a dominant genetic trait.

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