[Butterfly-shaped dystrophy of the macula (author's transl)]

The authors report a rare form of pigment dystrophy of the macula in a 17-years-old patient, which was diagnosed on the basis of characteristic ophthalmoscopic changes. Results obtained from an analysis of all the patients relations pointed to a familial occurrence of these changes. Up till now a similar case has been described only by Deutman and co-workers (1970) as "Butterfly-shaped pigment dystrophy of the fovea".