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C Jakobs

Showing results (141-150 of 417) with videos related to

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Molecular Genetics and Metabolism|August 18, 2001
Valproate induces in vitro accumulation of long-chain fatty acylcarnitinesM F Silva, C Jakobs, M Duran, et al.
Journal of Lipid Research|November 28, 1997
Phytanic acid alpha-oxidation: decarboxylation of 2-hydroxyphytanoyl-CoA to pristanic acid in human liverN M Verhoeven, R J Wanders, D S Schor, et al.
Investigative Ophthalmology & Visual Science|August 12, 2018
Ultrastructural Morphology of the Optic Nerve Head in Aged and Glaucomatous MiceYing Zhu, Anthony C Pappas, Rui Wang, et al.
Journal of Inherited Metabolic Disease|March 14, 2009
Measurement of D: -2-hydroxyglutarate dehydrogenase activity in cell homogenates derived from D: -2-hydroxyglutaric aciduria patientsW V Wickenhagen, G S Salomons, K M Gibson, et al.
FEBS Letters|April 20, 2001
Increased alpha3-fucosylation of alpha(1)-acid glycoprotein in patients with congenital disorder of glycosylation type IA (CDG-Ia)W Van Dijk, C Koeleman, B Van het Hof, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|December 1, 1978
Organic acid excretion in a patient with 3-hydroxy-3-methylglutaryl-CoA lyase deficiency: facts and artefactsM Duran, D Ketting, S K Wadman, et al.
Clinical Chemistry|September 1, 1993
Diagnosis of peroxisomal disorders by analysis of phytanic and pristanic acids in stored blood spots collected at neonatal screeningH J ten Brink, C M van den Heuvel, E Christensen, et al.
Journal of Inherited Metabolic Disease|January 1, 1996
Medium-chain triglyceride loading has no diagnostic power in long-chain 3-hydroxyacyl-CoA dehydrogenase deficiencyC G Costa, I T de Almeida, C Jakobs, et al.
Biochimica Et Biophysica Acta|May 8, 1992
Characteristics and subcellular localization of pristanoyl-CoA synthetase in rat liverR J Wanders, S Denis, C W van Roermund, et al.
Journal of Inherited Metabolic Disease|November 20, 1998
Studies on the oxidation of phytanic acid and pristanic acid in human fibroblasts by acylcarnitine analysisN M Verhoeven, C Jakobs, H J ten Brink, et al.
Pageof 42

Showing results (141-150 of 417) with videos related to

Sort By:
Pageof 42
Molecular Genetics and Metabolism|August 18, 2001
Valproate induces in vitro accumulation of long-chain fatty acylcarnitinesM F Silva, C Jakobs, M Duran, et al.
Journal of Lipid Research|November 28, 1997
Phytanic acid alpha-oxidation: decarboxylation of 2-hydroxyphytanoyl-CoA to pristanic acid in human liverN M Verhoeven, R J Wanders, D S Schor, et al.
Investigative Ophthalmology & Visual Science|August 12, 2018
Ultrastructural Morphology of the Optic Nerve Head in Aged and Glaucomatous MiceYing Zhu, Anthony C Pappas, Rui Wang, et al.
Journal of Inherited Metabolic Disease|March 14, 2009
Measurement of D: -2-hydroxyglutarate dehydrogenase activity in cell homogenates derived from D: -2-hydroxyglutaric aciduria patientsW V Wickenhagen, G S Salomons, K M Gibson, et al.
FEBS Letters|April 20, 2001
Increased alpha3-fucosylation of alpha(1)-acid glycoprotein in patients with congenital disorder of glycosylation type IA (CDG-Ia)W Van Dijk, C Koeleman, B Van het Hof, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|December 1, 1978
Organic acid excretion in a patient with 3-hydroxy-3-methylglutaryl-CoA lyase deficiency: facts and artefactsM Duran, D Ketting, S K Wadman, et al.
Clinical Chemistry|September 1, 1993
Diagnosis of peroxisomal disorders by analysis of phytanic and pristanic acids in stored blood spots collected at neonatal screeningH J ten Brink, C M van den Heuvel, E Christensen, et al.
Journal of Inherited Metabolic Disease|January 1, 1996
Medium-chain triglyceride loading has no diagnostic power in long-chain 3-hydroxyacyl-CoA dehydrogenase deficiencyC G Costa, I T de Almeida, C Jakobs, et al.
Biochimica Et Biophysica Acta|May 8, 1992
Characteristics and subcellular localization of pristanoyl-CoA synthetase in rat liverR J Wanders, S Denis, C W van Roermund, et al.
Journal of Inherited Metabolic Disease|November 20, 1998
Studies on the oxidation of phytanic acid and pristanic acid in human fibroblasts by acylcarnitine analysisN M Verhoeven, C Jakobs, H J ten Brink, et al.
Pageof 42