Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Filters

Carlo Viscomi

Showing results (21-30 of 101) with videos related to

Pageof 11
Sort By:
Mitochondrion|December 21, 2010
Hypoxic and hypercapnic challenges unveil respiratory vulnerability of Surf1 knockout mice, an animal model of Leigh syndromeGeorg M Stettner, Carlo Viscomi, Massimo Zeviani, et al.
The Journal of Biological Chemistry|August 5, 2004
Interaction of the pacemaker channel HCN1 with filamin ABiagio Gravante, Andrea Barbuti, Raffaella Milanesi, et al.
Nature Reviews. Drug Discovery|April 27, 2023
Opportunities for mitochondrial disease gene therapyCarlo Viscomi, Jelle van den Ameele, Kathrin C Meyer, et al.
Molecular Therapy. Methods & Clinical Development|June 2, 2020
A Single Intravenous Injection of AAV-PHP.B-<i>hNDUFS4</i> Ameliorates the Phenotype of <i>Ndufs4</i> <sup></sup> MicePedro Silva-Pinheiro, Raffaele Cerutti, Marta Luna-Sanchez, et al.
European Journal of Neurology|June 1, 2026
Letter to the Editor: Gastrointestinal Pseudo-Obstruction Is Not an Uncommon Phenotypic Manifestation of POLG1 Variants-Authors' ReplyGiuliana Capece, Renzo Manara, Leonardo Salviati, et al.
EMBO Molecular Medicine|August 21, 2012
Effective AAV-mediated gene therapy in a mouse model of ethylmalonic encephalopathyIvano Di Meo, Alberto Auricchio, Costanza Lamperti, et al.
Bioscience Reports|June 27, 2013
Proteome adaptations in Ethe1-deficient mice indicate a role in lipid catabolism and cytoskeleton organization via post-translational protein modificationsTatjana M Hildebrandt, Ivano Di Meo, Massimo Zeviani, et al.
Antioxidants & Redox Signaling|September 4, 2010
Chronic exposure to sulfide causes accelerated degradation of cytochrome c oxidase in ethylmalonic encephalopathyIvano Di Meo, Gigliola Fagiolari, Alessandro Prelle, et al.
Nature Reviews. Neurology|October 18, 2022
Gene therapy for primary mitochondrial diseases: experimental advances and clinical challengesMicol Falabella, Michal Minczuk, Michael G Hanna, et al.
Human Molecular Genetics|January 7, 2009
Paroxysmal non-kinesigenic dyskinesia is caused by mutations of the MR-1 mitochondrial targeting sequenceDaniele Ghezzi, Carlo Viscomi, Alessandra Ferlini, et al.
Pageof 11

Showing results (21-30 of 101) with videos related to

Sort By:
Pageof 11
Mitochondrion|December 21, 2010
Hypoxic and hypercapnic challenges unveil respiratory vulnerability of Surf1 knockout mice, an animal model of Leigh syndromeGeorg M Stettner, Carlo Viscomi, Massimo Zeviani, et al.
The Journal of Biological Chemistry|August 5, 2004
Interaction of the pacemaker channel HCN1 with filamin ABiagio Gravante, Andrea Barbuti, Raffaella Milanesi, et al.
Nature Reviews. Drug Discovery|April 27, 2023
Opportunities for mitochondrial disease gene therapyCarlo Viscomi, Jelle van den Ameele, Kathrin C Meyer, et al.
Molecular Therapy. Methods & Clinical Development|June 2, 2020
A Single Intravenous Injection of AAV-PHP.B-<i>hNDUFS4</i> Ameliorates the Phenotype of <i>Ndufs4</i> <sup></sup> MicePedro Silva-Pinheiro, Raffaele Cerutti, Marta Luna-Sanchez, et al.
European Journal of Neurology|June 1, 2026
Letter to the Editor: Gastrointestinal Pseudo-Obstruction Is Not an Uncommon Phenotypic Manifestation of POLG1 Variants-Authors' ReplyGiuliana Capece, Renzo Manara, Leonardo Salviati, et al.
EMBO Molecular Medicine|August 21, 2012
Effective AAV-mediated gene therapy in a mouse model of ethylmalonic encephalopathyIvano Di Meo, Alberto Auricchio, Costanza Lamperti, et al.
Bioscience Reports|June 27, 2013
Proteome adaptations in Ethe1-deficient mice indicate a role in lipid catabolism and cytoskeleton organization via post-translational protein modificationsTatjana M Hildebrandt, Ivano Di Meo, Massimo Zeviani, et al.
Antioxidants & Redox Signaling|September 4, 2010
Chronic exposure to sulfide causes accelerated degradation of cytochrome c oxidase in ethylmalonic encephalopathyIvano Di Meo, Gigliola Fagiolari, Alessandro Prelle, et al.
Nature Reviews. Neurology|October 18, 2022
Gene therapy for primary mitochondrial diseases: experimental advances and clinical challengesMicol Falabella, Michal Minczuk, Michael G Hanna, et al.
Human Molecular Genetics|January 7, 2009
Paroxysmal non-kinesigenic dyskinesia is caused by mutations of the MR-1 mitochondrial targeting sequenceDaniele Ghezzi, Carlo Viscomi, Alessandra Ferlini, et al.
Pageof 11