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Journal of Inherited Metabolic Disease
|
September 6, 2017
Triheptanoin versus trioctanoin for long-chain fatty acid oxidation disorders: a double blinded, randomized controlled trial
Melanie B Gillingham, Stephen B Heitner, Julie Martin, et al.
JCI Insight
|
April 8, 2026
Corrigendum to: Mitochondrial bioenergetics and cardiolipin remodeling abnormalities in mitochondrial trifunctional protein deficiency
Eduardo Vieira Neto, Meicheng Wang, Austin J Szuminsky, et al.
Molecular Genetics and Metabolism
|
May 19, 2023
Clinical, biochemical and molecular characterization of 12 patients with pyruvate carboxylase deficiency treated with triheptanoin
M Laura Duque Lasio, Angela C Leshinski, Nicole H Ducich, et al.
Neurology
|
January 4, 2020
Safety and efficacy of omaveloxolone in patients with mitochondrial myopathy: MOTOR trial
Karen L Madsen, Astrid E Buch, Bruce H Cohen, et al.
Nature Metabolism
|
September 28, 2023
Efficacy and safety of a synthetic biotic for treatment of phenylketonuria: a phase 2 clinical trial
Jerry Vockley, Neal Sondheimer, Marja Puurunen, et al.
Molecular Genetics and Metabolism
|
December 29, 2022
Synthetic mRNA rescues very long-chain acyl-CoA dehydrogenase deficiency in patient fibroblasts and a murine model
Xue-Jun Zhao, Ai-Walid Mohsen, Stephanie Mihalik, et al.
JAMA Pediatrics
|
February 15, 2021
Novel Variant Findings and Challenges Associated With the Clinical Integration of Genomic Testing: An Interim Report of the Genomic Medicine for Ill Neonates and Infants (GEMINI) Study
Jill L Maron, Stephen F Kingsmore, Kristen Wigby, et al.
Human Genetics
|
June 5, 2008
The ACADS gene variation spectrum in 114 patients with short-chain acyl-CoA dehydrogenase (SCAD) deficiency is dominated by missense variations leading to protein misfolding at the cellular level
Christina B Pedersen, Steen Kølvraa, Agnete Kølvraa, et al.
Nature Metabolism
|
July 23, 2021
Safety and pharmacodynamics of an engineered E. coli Nissle for the treatment of phenylketonuria: a first-in-human phase 1/2a study
Marja K Puurunen, Jerry Vockley, Shawn L Searle, et al.
JAMA
|
July 11, 2023
Rapid Whole-Genomic Sequencing and a Targeted Neonatal Gene Panel in Infants With a Suspected Genetic Disorder
Jill L Maron, Stephen Kingsmore, Bruce D Gelb, et al.
Page
of 30
Search research articles
Search
Showing results (251-260 of 295) with videos related to
Sort By:
Page
of 30
Journal of Inherited Metabolic Disease
|
September 6, 2017
Triheptanoin versus trioctanoin for long-chain fatty acid oxidation disorders: a double blinded, randomized controlled trial
Melanie B Gillingham, Stephen B Heitner, Julie Martin, et al.
JCI Insight
|
April 8, 2026
Corrigendum to: Mitochondrial bioenergetics and cardiolipin remodeling abnormalities in mitochondrial trifunctional protein deficiency
Eduardo Vieira Neto, Meicheng Wang, Austin J Szuminsky, et al.
Molecular Genetics and Metabolism
|
May 19, 2023
Clinical, biochemical and molecular characterization of 12 patients with pyruvate carboxylase deficiency treated with triheptanoin
M Laura Duque Lasio, Angela C Leshinski, Nicole H Ducich, et al.
Neurology
|
January 4, 2020
Safety and efficacy of omaveloxolone in patients with mitochondrial myopathy: MOTOR trial
Karen L Madsen, Astrid E Buch, Bruce H Cohen, et al.
Nature Metabolism
|
September 28, 2023
Efficacy and safety of a synthetic biotic for treatment of phenylketonuria: a phase 2 clinical trial
Jerry Vockley, Neal Sondheimer, Marja Puurunen, et al.
Molecular Genetics and Metabolism
|
December 29, 2022
Synthetic mRNA rescues very long-chain acyl-CoA dehydrogenase deficiency in patient fibroblasts and a murine model
Xue-Jun Zhao, Ai-Walid Mohsen, Stephanie Mihalik, et al.
JAMA Pediatrics
|
February 15, 2021
Novel Variant Findings and Challenges Associated With the Clinical Integration of Genomic Testing: An Interim Report of the Genomic Medicine for Ill Neonates and Infants (GEMINI) Study
Jill L Maron, Stephen F Kingsmore, Kristen Wigby, et al.
Human Genetics
|
June 5, 2008
The ACADS gene variation spectrum in 114 patients with short-chain acyl-CoA dehydrogenase (SCAD) deficiency is dominated by missense variations leading to protein misfolding at the cellular level
Christina B Pedersen, Steen Kølvraa, Agnete Kølvraa, et al.
Nature Metabolism
|
July 23, 2021
Safety and pharmacodynamics of an engineered E. coli Nissle for the treatment of phenylketonuria: a first-in-human phase 1/2a study
Marja K Puurunen, Jerry Vockley, Shawn L Searle, et al.
JAMA
|
July 11, 2023
Rapid Whole-Genomic Sequencing and a Targeted Neonatal Gene Panel in Infants With a Suspected Genetic Disorder
Jill L Maron, Stephen Kingsmore, Bruce D Gelb, et al.
Page
of 30