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R J Wanders

Showing results (161-170 of 497) with videos related to

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American Journal of Human Genetics|May 1, 1996
Molecular characterization of mitochondrial trifunctional protein deficiency: formation of the enzyme complex is important for stabilization of both alpha- and beta-subunitsS Ushikubo, T Aoyama, T Kamijo, et al.
Genomics|April 1, 1996
3-Hydroxy-3-methylglutaryl CoA lyase (HL): mouse and human HL gene (HMGCL) cloning and detection of large gene deletions in two unrelated HL-deficient patientsS P Wang, M F Robert, K M Gibson, et al.
Biological Psychiatry|March 21, 2001
Significantly reduced docosahexaenoic and docosapentaenoic acid concentrations in erythrocyte membranes from schizophrenic patients compared with a carefully matched control groupJ Assies, R Lieverse, P Vreken, et al.
Journal of Inherited Metabolic Disease|July 17, 1999
X-linked cardioskeletal myopathy and neutropenia (Barth syndrome) (MIM 302060)P G Barth, R J Wanders, P Vreken, et al.
Journal of Inherited Metabolic Disease|August 1, 1998
Bifunctional protein deficiency: complementation within the same group suggesting differential enzyme defects and clues to the underlying basisE G Van Grunsven, E van Berkel, H Lemonde, et al.
Biochimica Et Biophysica Acta|May 8, 1992
Characteristics and subcellular localization of pristanoyl-CoA synthetase in rat liverR J Wanders, S Denis, C W van Roermund, et al.
Journal of Inherited Metabolic Disease|November 20, 1998
Studies on the oxidation of phytanic acid and pristanic acid in human fibroblasts by acylcarnitine analysisN M Verhoeven, C Jakobs, H J ten Brink, et al.
Journal of Inherited Metabolic Disease|October 8, 1998
Lactic acidosis in long-chain fatty acid beta-oxidation disordersF V Ventura, J P Ruiter, L IJlst, et al.
European Journal of Pediatrics|October 1, 1994
Long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency: a severe fatty acid oxidation disorderA C Sewell, S W Bender, S Wirth, et al.
The Journal of Biological Chemistry|May 30, 1998
Alkyl-dihydroxyacetonephosphate synthase. Fate in peroxisome biogenesis disorders and identification of the point mutation underlying a single enzyme deficiencyE C de Vet, L Ijlst, W Oostheim, et al.
Pageof 50

Showing results (161-170 of 497) with videos related to

Sort By:
Pageof 50
American Journal of Human Genetics|May 1, 1996
Molecular characterization of mitochondrial trifunctional protein deficiency: formation of the enzyme complex is important for stabilization of both alpha- and beta-subunitsS Ushikubo, T Aoyama, T Kamijo, et al.
Genomics|April 1, 1996
3-Hydroxy-3-methylglutaryl CoA lyase (HL): mouse and human HL gene (HMGCL) cloning and detection of large gene deletions in two unrelated HL-deficient patientsS P Wang, M F Robert, K M Gibson, et al.
Biological Psychiatry|March 21, 2001
Significantly reduced docosahexaenoic and docosapentaenoic acid concentrations in erythrocyte membranes from schizophrenic patients compared with a carefully matched control groupJ Assies, R Lieverse, P Vreken, et al.
Journal of Inherited Metabolic Disease|July 17, 1999
X-linked cardioskeletal myopathy and neutropenia (Barth syndrome) (MIM 302060)P G Barth, R J Wanders, P Vreken, et al.
Journal of Inherited Metabolic Disease|August 1, 1998
Bifunctional protein deficiency: complementation within the same group suggesting differential enzyme defects and clues to the underlying basisE G Van Grunsven, E van Berkel, H Lemonde, et al.
Biochimica Et Biophysica Acta|May 8, 1992
Characteristics and subcellular localization of pristanoyl-CoA synthetase in rat liverR J Wanders, S Denis, C W van Roermund, et al.
Journal of Inherited Metabolic Disease|November 20, 1998
Studies on the oxidation of phytanic acid and pristanic acid in human fibroblasts by acylcarnitine analysisN M Verhoeven, C Jakobs, H J ten Brink, et al.
Journal of Inherited Metabolic Disease|October 8, 1998
Lactic acidosis in long-chain fatty acid beta-oxidation disordersF V Ventura, J P Ruiter, L IJlst, et al.
European Journal of Pediatrics|October 1, 1994
Long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency: a severe fatty acid oxidation disorderA C Sewell, S W Bender, S Wirth, et al.
The Journal of Biological Chemistry|May 30, 1998
Alkyl-dihydroxyacetonephosphate synthase. Fate in peroxisome biogenesis disorders and identification of the point mutation underlying a single enzyme deficiencyE C de Vet, L Ijlst, W Oostheim, et al.
Pageof 50