Showing results (1-10 of 217) with videos related to
Sort By:
Pageof 22
Biochimica Et Biophysica Acta|June 6, 2000
Characterization of two alpha-galactosidase mutants (Q279E and R301Q) found in an atypical variant of Fabry diseaseR Kase, U Bierfreund, A Klein, et al.FEBS Letters|September 9, 1996
Only sphingolipid activator protein B (SAP-B or saposin B) stimulates the degradation of globotriaosylceramide by recombinant human lysosomal alpha-galactosidase in a detergent-free liposomal systemR Kase, U Bierfreund, A Klein, et al.Die Naturwissenschaften|September 1, 1995
[Glycolipids of the cell surface--biochemistry of their decomposition]K Sandhoff, T KolterBrain Pathology (Zurich, Switzerland)|February 11, 1998
Recent advances in the biochemistry of sphingolipidosesT Kolter, K SandhoffJournal of Inherited Metabolic Disease|September 5, 1998
Glycosphingolipid degradation and animal models of GM2-gangliosidosesT Kolter, K SandhoffActa Biochimica Polonica|November 20, 1998
Processing of sphingolipid activator proteins and the topology of lysosomal digestionK Sandhoff, T KolterClinica Chimica Acta; International Journal of Clinical Chemistry|January 22, 1998
Biochemistry of glycosphingolipid degradationK Sandhoff, T KolterBiochimica Et Biophysica Acta|November 9, 2000
Quantification of mRNAs encoding proteins of the glycosphingolipid catabolism in mouse models of GM2 gangliosidoses and sphingolipid activator protein precursor (prosaposin) deficiencyA Potratz, S Hüttler, U Bierfreund, et al.Annals of the New York Academy of Sciences|July 21, 1998
Sphingolipid metabolism. Sphingoid analogs, sphingolipid activator proteins, and the pathology of the cellK Sandhoff, T Kolter, G Van Echten-DeckertPageof 22