[Pancreatic vascular tumours of childhood: a heterogeneous nosologic spectrum]

Infantile pancreatic vascular tumors are very unusual and are described with an old and imprecise terminology. We report two new cases in 2 and 4 months old children, the first one associated with Kasabach-Merritt syndrome, the second revealed by cholestasis. The histology diagnosis was kaposiform hemangioendothelioma and juvenile capillary hemangioma respectively. Outcome was favourable after selective embolization for one and biliary derivation for the other. These case reports show that infantile vascular pancreatic tumors form a heterogeneous group. Most of them would be in fact kaposiform hemangioendothelioma with a benign behavior, in contrast with aggressive growth for retroperitoneal localizations.