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Published on: July 18, 2014
Congenitally corrected transposition of the great arteries treated by partial systemic ventriculectomy
Ayaka Kobashi1, Michihiro Suwa, Tomomi Nakamura
1The Third Division, Department of Internal Medicine, Osaka Medical College, Takatsuki City, Japan.
Insights
Congenitally corrected transposition of the great arteries (CCTGA) can lead to systemic ventricular dysfunction in adults. This case report details a partial ventriculectomy performed for this condition.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Congenitally corrected transposition of the great arteries (CCTGA) involves atrioventricular and ventriculo-arterial discordance.
- The left ventricle typically supports pulmonary circulation, and the right ventricle supports systemic circulation in CCTGA.
- Systemic ventricular dysfunction is a frequent complication in older CCTGA patients, irrespective of other defects.
Observation:
- A patient with CCTGA presented with systemic ventricular dysfunction.
- The patient underwent a partial ventriculectomy procedure.
Findings:
- Partial ventriculectomy was performed as a treatment for systemic ventricular dysfunction in a patient with CCTGA.
- This intervention addresses a known complication of CCTGA.
Implications:
- Partial ventriculectomy may be a viable surgical option for managing systemic ventricular dysfunction in CCTGA.
- Further research is warranted to evaluate the long-term efficacy and outcomes of this procedure in CCTGA patients.
Abstract:
Congenitally corrected transposition of the great arteries (CCTGA) is a rare congenital heart disease characterized by atrioventricular (AV) and ventriculo-arterial discordance;(1) that is, the left ventricle supports the pulmonary circulation and the right ventricle supports the systemic circulation. The most common cardiac anomalies in CCTGA include ventricular septal defect, pulmonary outflow tract obstruction and abnormalities of the systemic AV valve. (1) The dysfunction of the systemic ventricle occurs with increasing frequency in older patients with CCTGA, independent of their commonly associated structural defects.(2-4) We report a patient with CCTGA undergone the partial ventriculectomy for his systemic ventricular dysfunction.
