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Death from chronic tonsillar herniation in a patient with lumboperitoneal shunt and Crouzon's disease
P D Chumas1, J M Drake, M R Del Bigio
1Division of Neurosurgery, Hospital for Sick Children, University of Toronto, Ontario, Canada.
British Journal of Neurosurgery
|January 1, 1992
Abstract:
A 2.5-year-old girl with Crouzon's disease, hydrocephalus, and a lumboperitoneal shunt died as a result of chronic tonsillar herniation (acquired Chiari 'malformation'). The possible synergistic role of the cranial dysmorphism and the lumboperitoneal shunt in the development of this anomaly is discussed. The literature is reviewed and it is argued that if hydrocephalus occurs in infants in whom cephalocranial disproportion is likely to develop, then it is inadvisable to insert a lumboperitoneal shunt.