Persistent fifth aortic arch and fourth arch interruption in a 28-year-old woman
Y Isomatsu1, Y Takanashi, M Terada
1Division of Cardiovascular Surgery, Department of Surgery, Yokohama City University School of Medicine, Yokohama, Japan. isomatsu@med.yokohama-cu.ac.jp
Pediatric Cardiology
|January 27, 2004
Summary
A surgical repair successfully treated a rare congenital heart defect involving aortic arch anomalies in a young woman. The procedure used graft interposition to correct aortic coarctation and a persistent fifth aortic arch.
Area of Science:
- Cardiovascular Surgery
- Congenital Heart Disease
- Medical Imaging
Background:
- Persistent fifth aortic arch is a rare congenital anomaly.
- Aortic coarctation presents a significant risk of cardiovascular complications.
- Surgical intervention is often necessary for complex aortic arch abnormalities.
Observation:
- A 28-year-old woman presented with a unique combination of persistent fifth aortic arch and aortic coarctation.
- The aortic coarctation was associated with an interruption of the fourth aortic arch.
- No other congenital cardiac malformations were identified.
Findings:
- The patient underwent successful graft interposition surgery.
- A 20 mm diameter graft was used to connect the fourth aortic arch (including the left subclavian artery) to the descending aorta.
- This effectively reconstructed the aortic arch continuity.
Implications:
- This case highlights a successful surgical strategy for a complex aortic arch malformation.
- The findings contribute to the understanding of managing rare congenital cardiovascular conditions.
- Successful surgical repair can lead to improved long-term outcomes for patients with aortic arch anomalies.
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