Aortic valve papillary fibroelastoma

Wlodzimierz Kuroczynski1, Ulrich Hake, Diethard Pruefer

  • 1Department of Cardiothoracic and Vascular Surgery, Johannes Gutenberg-University, Mainz, Germany. kuroczynski@uni-mainz.de

Insights

Cardiac papillary fibroelastoma (CPF), a rare benign heart tumor, is increasingly diagnosed with echocardiography. Surgical removal is effective for CPF, preventing potential cardiac or cerebrovascular ischemia.

Area of Science:

  • Cardiology
  • Oncology

Background:

  • Cardiac papillary fibroelastoma (CPF) is a rare, benign primary cardiac tumor.
  • It is the third most common primary cardiac tumor and the most frequent tumor of the valvular endothelium.
  • Historically diagnosed post-mortem or incidentally during surgery, CPF is now detectable in living patients.

Observation:

  • Transthoracic echocardiography (TTE) and transesophageal echocardiography (TEE) enable in vivo diagnosis of CPF.
  • CPF can lead to cerebrovascular or cardiac ischemia through embolization or vascular ostia occlusion.
  • Emboli may originate from tumor fragments or associated thrombus.

Findings:

  • The study reports a case of aortic valve CPF diagnosed via TEE.
  • Surgical excision of the aortic valve CPF was successfully performed.

Implications:

  • Early diagnosis of CPF using advanced echocardiography is crucial.
  • Surgical intervention for CPF can prevent serious embolic complications.
  • This case highlights the importance of TEE in diagnosing and managing CPF.

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