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Multiple cutaneous angiomas and Poems syndrome
Brigitte Granel1, Jacques Serratrice, Christine de Roux-Serratrice
1Service de Médecine Interne, Hôpital de la Timone, Marseille.
Presse Medicale (Paris, France : 1983)
|March 22, 2006
Summary
Poems syndrome, a rare condition, was diagnosed in a patient presenting with unusual skin angiomas. Prompt steroid treatment improved symptoms, highlighting this rare cutaneous manifestation.
Area of Science:
- Medicine
- Oncology
- Neurology
Background:
- Poems syndrome is a rare multisystem disorder.
- It is characterized by polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy (M-proteins), and skin lesions.
Observation:
- A case study details a patient with bone plasmocytoma and polyneuropathy.
- The patient developed diffuse cutaneous angiomas, prompting the diagnosis of Poems syndrome.
Findings:
- The patient exhibited additional Poems syndrome features: endocrine dysfunction, sclerotic bone lesions, monoclonal gammopathy, and anasarca.
- Steroid therapy resulted in significant improvement of polyserositis.
Implications:
- This case highlights diffuse cutaneous angiomas as an unusual manifestation of Poems syndrome.
- Early diagnosis and treatment, including steroids, can lead to a good outcome.
- Recognizing rare cutaneous signs is crucial for diagnosing complex syndromes like Poems.
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