Related Experiment Video
Updated: Jul 19, 2026

Echocardiographic Evaluation of Atrial Communications before Transcatheter Closure
Published on: February 8, 2022
Non-compaction of the right atrium and left ventricle in Ebstein's malformation
Claudia Stöllberger1, Wolfgang Kopsa, Josef Finsterer
1Second Medical Department, Krankenanstalt Rudolfstiftung, Vienna, Austria. claudia.stoellberger@chello.at
Abstract:
Ebstein's malformation (EM) is characterized by dysplasia and displacement of the tricuspid inferior and septal leaflets from the true atrioventricular (AV) junction. Left ventricular hypertrabeculation/non-compaction (LVHT) including the 'atrialized' portion in EM has not been described. A 42-year-old man with a history of radiofrequency ablation of a Mahaim-like bundle suffered from chest pain. Coronary angiography was normal, but echocardiography showed a septal tricuspid leaflet inserting 3.5-cm apically beyond the AV junction, deep recesses of the atrialized interventricular septum, and a heavily trabeculated left ventricle; these were confirmed by cardiac magnetic resonance imaging. Neurologically, hypoacusis, positive pyramidal signs, postural tremor and brisk tendon reflexes were identified.
Related Concept Videos
Chambers of the Heart
Deoxygenated blood from the body is received in the right...
Mitral Stenosis I: Introduction
Mitral Regurgitation I: Introduction
Aortic Regurgitation I: Introduction
Cardiomyopathy III: Hypertrophic Cardiomyopathy
Development of the Heart
As the embryo undergoes lateral folding, these paired tubes approach each other, merging into a single primitive heart tube by...

