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Urinary 3'5' cyclic AMP. Diagnostic test in pseudohypoparathyroidism.
Archives of Disease in Childhood
|August 1, 1975
Summary
Pseudohypoparathyroidism diagnosis can be aided by measuring urinary cyclic AMP (adenosine 3'5'-cyclic phosphate) levels. In pseudohypoparathyroidism patients, parathyroid hormone infusion did not increase cyclic AMP, unlike in healthy individuals.
Area of Science:
- Biochemistry
- Pediatric Endocrinology
- Metabolic Disorders
Background:
- Pseudohypoparathyroidism is a genetic disorder characterized by resistance to parathyroid hormone.
- Calcium and phosphorus metabolism are significantly affected in pseudohypoparathyroidism.
- Urinary cyclic AMP is a key second messenger in parathyroid hormone signaling.