Transcatheter closure of ruptured sinus of Valsalva aneurysm causing Fontan circulation failure

Giuseppe Santoro1, Giuseppe Pacileo, Maurizio Cappelli Bigazzi

  • 1Division of Cardiology, Second University of Naples, Monaldi Hospital, Naples, Italy. santoropino@tin.it

Insights

A rare congenital sinus of Valsalva aneurysm ruptured into an accessory chamber, causing heart failure in a patient with tricuspid atresia. Percutaneous closure provided immediate clinical improvement.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Cardiac Surgery

Background:

  • Congenital sinus of Valsalva aneurysm (SVA) is a rare cardiac malformation.
  • Rupture of SVA typically leads to symptoms and can be misdiagnosed, especially with complex cardiac defects.

Observation:

  • A patient with tricuspid atresia, previously treated with a Fontan procedure, presented with rapidly progressive heart failure.
  • Echocardiography revealed a ruptured sinus of Valsalva aneurysm communicating with an accessory ventricular chamber.

Findings:

  • The rupture of the sinus of Valsalva aneurysm into the accessory ventricular chamber was the cause of the patient's heart failure.
  • Percutaneous implantation of an Amplatzer duct occluder successfully treated the ruptured aneurysm.

Implications:

  • This case highlights the importance of considering SVA rupture in patients with complex congenital heart disease and heart failure.
  • Percutaneous closure offers a minimally invasive treatment option for ruptured SVA, leading to rapid clinical improvement.