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Published on: December 11, 2017
Transcatheter closure of ruptured sinus of Valsalva aneurysm causing Fontan circulation failure
Giuseppe Santoro1, Giuseppe Pacileo, Maurizio Cappelli Bigazzi
1Division of Cardiology, Second University of Naples, Monaldi Hospital, Naples, Italy. santoropino@tin.it
Insights
A rare congenital sinus of Valsalva aneurysm ruptured into an accessory chamber, causing heart failure in a patient with tricuspid atresia. Percutaneous closure provided immediate clinical improvement.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Congenital sinus of Valsalva aneurysm (SVA) is a rare cardiac malformation.
- Rupture of SVA typically leads to symptoms and can be misdiagnosed, especially with complex cardiac defects.
Observation:
- A patient with tricuspid atresia, previously treated with a Fontan procedure, presented with rapidly progressive heart failure.
- Echocardiography revealed a ruptured sinus of Valsalva aneurysm communicating with an accessory ventricular chamber.
Findings:
- The rupture of the sinus of Valsalva aneurysm into the accessory ventricular chamber was the cause of the patient's heart failure.
- Percutaneous implantation of an Amplatzer duct occluder successfully treated the ruptured aneurysm.
Implications:
- This case highlights the importance of considering SVA rupture in patients with complex congenital heart disease and heart failure.
- Percutaneous closure offers a minimally invasive treatment option for ruptured SVA, leading to rapid clinical improvement.
Abstract:
Congenital sinus of Valsalva aneurysm is a rare cardiac malformation that usually becomes symptomatic as a consequence of intracardiac or extracardiac rupture. It is difficult to suspect in association with complex cardiac defects and its rupture may be misdiagnosed as progressive aortic regurgitation. This case report refers to a patient with tricuspid atresia submitted to Fontan procedure five years previously, in whom a sinus of Valsalva aneurysm rupture into the accessory ventricular chamber caused rapidly progressive heart failure. The malformation was suspected by echocardiography and treated by percutaneous implantation of an Amplatzer duct occluder, with immediate improvement of the patient's clinical and functional status.
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