Shone's Anomaly - A Case Report

Area of Science:

• Cardiology
• Congenital Heart Disease
• Cardiac Surgery

Background:

• Shone's anomaly is a rare congenital cardiac malformation characterized by multiple left heart obstructions.
• These obstructions include supravalvular mitral ring, parachute mitral valve, subaortic stenosis, and coarctation of the aorta.
• While presenting a spectrum of abnormalities, most patients can achieve satisfactory outcomes.

Purpose of the Study:

• To report a case of Shone's anomaly presenting in the third decade of life.
• To highlight the successful surgical management of a complex case.
• To emphasize the feasibility of multi-stage repair in a single sitting.

Main Methods:

• Surgical correction of multiple left heart obstructions.
• A two-stage operative approach was employed.
• The procedure was completed successfully in a single sitting.

Main Results:

• The patient, presenting in the third decade, underwent successful surgical correction.
• The two-stage procedure in a single sitting yielded a satisfactory outcome.
• Operative mortality and outcome are influenced by mitral valve disease severity and the number of procedures.

Conclusions:

• Shone's anomaly, despite its complexity, can be managed successfully with surgical intervention.
• A staged, single-sitting repair is a viable option for adult patients.
• Early and comprehensive surgical management is crucial for optimal outcomes in Shone's anomaly.