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[Acquired naevus flammeus (Fegeler syndrome)]
J T Kainz1, H P Soyer, S Strasser-Fuchs
1Universitätsklinik für Dermatologie und Venerologie Graz.
Abstract:
In contrast to common port-wine stains, acquired port-wine stains are extremely rare. We report on an acquired port-wine stain that evolved on the thigh of a 69-year-old male patient and was accompanied by lumbalgia on the same side. Impairment of vegetative nerve fibres by spinal root compression may be considered a causative factor in our patient.
Insights
Acquired port-wine stains are rare vascular malformations. This case study reports a unique instance in a 69-year-old male, potentially linked to nerve compression.
Area of Science:
- Dermatology
- Neurology
- Vascular Malformations
Background:
- Port-wine stains (PWS) are typically congenital vascular malformations.
- Acquired port-wine stains are exceptionally rare, with limited reported cases.
- Understanding the etiology of acquired PWS is crucial for diagnosis and management.
Observation:
- A 69-year-old male presented with an acquired port-wine stain on his thigh.
- The patient also experienced ipsilateral lumbalgia (lower back pain).
- This co-occurrence prompted an investigation into potential underlying causes.
Findings:
- The acquired port-wine stain developed later in life, differing from typical congenital PWS.
- The association with lumbalgia suggests a possible neurological link.
- Spinal root compression affecting vegetative nerve fibers is hypothesized as a causative factor.
Implications:
- This case expands the understanding of port-wine stain development.
- It highlights the potential role of neurological factors in acquired vascular lesions.
- Further research may elucidate the relationship between nerve impairment and acquired PWS.