Infantile digital fibromatosis
Helena O B Taylor1, Steven E Gellis, Birgitta A R Schmidt
1Department of Plastic Surgery, Children's Hospital and Harvard Medical School, Boston, Massachusetts 02115, USA.
Annals of Plastic Surgery
|September 25, 2008
Summary
Infantile digital fibromas, rare benign tumors in children, can appear after surgery. This case involved extensive post-surgical fibromas on all four extremities.
Area of Science:
- Pediatric Oncology
- Dermatopathology
Background:
- Infantile digital fibromas are rare, benign neoplasms primarily affecting children's digits.
- Diagnosis often requires biopsy due to resemblance to other skin lesions.
- These tumors are characterized by myofibroblasts with unique intracellular inclusions.
Observation:
- A 2-year-old patient developed extensive infantile digital fibromas across all four extremities.
- The fibromas appeared postsurgically following syndactyly release.
- The extent and post-surgical onset were highly unusual compared to typical presentations.
Findings:
- The case highlights a rare postsurgical manifestation of infantile digital fibromas.
- The extensive nature of the lesions in this patient is noteworthy.
- Myofibroblastic origin with pathognomonic inclusions confirmed the diagnosis.
Implications:
- This case expands the understanding of infantile digital fibroma presentation and potential triggers.
- It underscores the importance of considering digital fibromas in postsurgical pediatric cases.
- Further research may explore the link between surgical procedures and fibroma development.
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