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Standardized Technique of Aortic Valve Re-implantation for Valve-sparing Aortic Root Replacement
Published on: December 11, 2017
Aortic root reconstruction in a nine-year-old child: a case report
Zoltan Szabolcs1, Tivadar Hüttl, Laszlo Szudi
1Cardiovascular Surgery Department, Semmelweis University, Budapest, Hungary. szabzol51@t-online.hu
The Journal of Heart Valve Disease
|May 22, 2009
Summary
Marfan syndrome can cause aortic root dilatation in young children. A nine-year-old boy with severe aortic regurgitation and ascending aorta aneurysm underwent a Bentall procedure, highlighting early surgical intervention needs.
Area of Science:
- Cardiology
- Pediatric Surgery
- Genetics
Background:
- Marfan syndrome frequently causes aortic root dilatation by age five.
- Surgical intervention for aortic aneurysms and regurgitation is uncommon in children under ten.
Observation:
- A nine-year-old male patient presented with severe aortic regurgitation.
- Ascending aorta aneurysm measured 76.8 mm.
Findings:
- The patient underwent a Bentall procedure.
- Aortic valve sparing was not possible due to marked annular dilatation and abnormal valve cusps.
Implications:
- This case underscores the importance of early surveillance and potential surgical management for aortic complications in pediatric Marfan syndrome.
- Bentall procedure is a viable option for complex aortic root pathology in children.
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