Papillary cystadenocarcinoma of the lacrimal gland

A 35-year-old man complained of progressive exophthalmos on the left eye for six months. MRI revealed approximately 18 mm x 17 mm cyst neoplasm across the inner and outer muscle cone in the left orbital cavity. Extraction was performed. The cyst wall of the tumor had the infiltration of the cancer cells and contained the residual lacrimal gland tissue. The patient refused further cranio-orbital resection or preoperative/postoperative radiotherapy or chemotherapy. Following for nine years found no local recurrence or systemic metastasis.