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Melanotic neuroectodermal tumour of infancy
T H Siddiqui1, M R Amin, M A Bashar
1Department of Paediatric Surgery, Bangabandhu Sheikh Mujib Medical University, Shahbagh, Dhaka, Bangladesh. siddiqui_2000@yahoo.com
Mymensingh Medical Journal : MMJ
|April 28, 2011
Summary
Melanotic neuroectodermal tumour of infancy is a rare, benign pigmented neoplasm. Surgical excision offers an effective cure with no recurrence observed in this case.
Area of Science:
- Pediatric Oncology
- Dermatopathology
- Surgical Pathology
Background:
- Melanotic neuroectodermal tumour of infancy (NMT) is a rare, benign pigmented neoplasm of neural crest origin.
- Typically occurring in infants under one year of age, NMT most commonly affects the anterior maxillary alveolar ridge.
Observation:
- A case of NMT is presented in a 6-month-old male infant.
- The tumor presented as a blackish mass involving the right cheek and maxilla, extending into the maxillary sinuses.
Findings:
- Histological examination confirmed the diagnosis of NMT.
- Surgical excision via a sub-labial incision successfully removed the tumor.
- Post-operative follow-up for nearly one year showed no signs of recurrence.
Implications:
- This case highlights the importance of clinical awareness for pigmented soft tissue masses in children.
- Prompt diagnosis and surgical management are crucial for effective treatment and favorable outcomes.
- Reporting such cases aids in improving the understanding and therapeutic strategies for NMT.
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